脂肪细胞肿瘤(Adipocytic tumours)

良性(Benign)

  • 8850/0 脂肪瘤 NOS (Lipoma NOS)
  • 8856/0 肌内脂肪瘤(Intramuscular lipoma)
    软骨样脂肪瘤(Chondroid lipoma)
  • 脂肪瘤病(Lipomatosis)
    弥漫性脂肪瘤病(Diffuse lipomatosis)
    多发对称性脂肪瘤病(Multiple symmetrical lipomatosis)
    盆腔脂肪瘤病(Pelvic lipomatosis)
    类固醇脂肪瘤病 (Steroid lipomatosis)
    HIV脂肪代谢障碍 (HIV lipodystrophy)
  • 神经脂肪瘤病 (Lipomatosis of nerve)
  • 8881/0 脂肪母细胞瘤/脂肪母细胞瘤病 (Lipoblastomatosis)
    局限性(脂肪母细胞瘤) (Localized (lipoblastoma))
    弥漫性(脂肪母细胞瘤病) (Diffuse (lipoblastomatosis))
  • 8861/0 血管脂肪瘤NOS (Angiolipoma NOS)
    富于细胞性血管脂肪瘤 (Cellular angiolipoma)
  • 8890/0 软组织肌脂肪瘤(Myolipoma)
  • 8862/0 软骨样脂肪瘤 (Chondroid lipoma)
  • 8857/0 梭形细胞脂肪瘤(Spindle cell lipoma)
  • 8857/0 非典型梭形细胞/多形性脂肪瘤样肿瘤(Atypical spindle cell/pleomorphic lipomatous tumour)
  • 8880/0 冬眠瘤(Hibernoma）

中间性(局部侵袭性)Intermediate (locally aggressive)

  • 8850/1 非典型性脂肪瘤样肿瘤( Atypical lipomatous tumour)

恶性(Malignant)

  • 8851/3 脂肪肉瘤，高分化，NOS (Liposarcoma, well-differentiated, NOS)
    8851/3 脂肪瘤样脂肪肉瘤(Lipoma-like liposarcoma)
    8851/3 炎症性脂肪肉瘤(Inflammatory liposarcoma)
    8851/3 硬化性脂肪肉瘤(Sclerosing liposarcoma)
  • 8858/3 去分化脂肪肉瘤(Dedifferentiated liposarcoma)
  • 8852/3 黏液样脂肪肉瘤(Myxoid liposarcoma)
  • 8854/3 多形性脂肪肉瘤(Pleomorphic liposarcoma)
    上皮样脂肪肉瘤(Epithelioid liposarcoma)
  • 8859/3 黏液样多形性脂肪肉瘤(Myxoid pleomorphic liposarcoma)

纤维母细胞/肌纤维母细胞性肿瘤(Fibroblastic and myofibroblastic tumours)

良性(Benign)

  • 8828/0 结节性筋膜炎(Nodular fasciitis)
    血管内筋膜炎(Intravascular fasciitis)
    颅骨筋膜炎(Cranial fasciitis)
  • 8828/0 增生性筋膜炎(Proliferative fascitis)
  • 8828/0 增生性肌炎(Proliferative myositis)
  • 骨化性肌炎和指趾纤维骨性假瘤(Myositis ossificans and fibro-osseous pseudotumour of digits)
  • 缺血性筋膜炎(Ischaemic fasciitis)
  • 8820/0 弹力纤维瘤(Elastofibroma)
  • 8992/0 婴儿纤维性错构瘤(Fibrous hamartoma of infancy)
  • 结肠纤维瘤病(Fibromatosis colli)
  • 幼年性玻璃样变纤维瘤病(Juvenile hyaline fibromatosis)
  • 包涵体性纤维瘤病(Inclusion body fibromatosis)
  • 8813/0 腱鞘纤维瘤(Fibroma of tendon sheath)
  • 8810/0 促结缔组织增生性纤维母细胞瘤(Desmoplastic fibroblastoma)
  • 8825/0 肌纤维母细胞瘤(Myofibroblastoma)
  • 8816/0 钙化性腱膜纤维瘤(Calcifying aponeurotic fibroma)
  • EWSRI-SMAD3阳性纤维母细胞性肿瘤(EWSR1-SMAD3-positive fibroblastic tumour(emerging))
  • 8826/0 血管肌纤维母细胞瘤(Angiomyofibroblastoma)
  • 9160/0 富于细胞性血管纤维瘤(Celular angiofibroma)
  • 9160/0 血管纤维瘤NOS (Angiofibroma NOS)
  • 8810/0 项型纤维瘤(Nuchal fibroma)
  • 8811/0 肢端纤维黏液瘤(Acral fibromyxoma)
  • 8810/0 Gardner纤维瘤(Gardner fibroma)

中间性(局部侵袭性)Intermediate (locally aggressive)

  • 8815/0 孤立性纤维性肿瘤，良性(Solitary fibrous tumour, benign)
  • 8813/1 掌/跖纤维瘤病(Palmar/plantar-type fibromatosis)
  • 8821/1 韧带样纤维瘤病(Desmoid-type fibromatosis)
    8821/1 腹壁外韧带样纤维瘤病(Extra-abdominal desmoid fibromatosis)
    8822/1 腹壁纤维瘤病(Abdominal fibromatosis)
  • 8851/1 脂肪纤维瘤病(Lipofibromatosis)
  • 8834/1 巨细胞纤维母细胞瘤(Giant cell fibroblastoma)

中间性(偶有转移性)Intermediate(rarely metastasizing)

  • 8832/1 隆突性皮肤纤维肉瘤NOS (Dermatofibrosarcoma protuberans NOS)
    8833/1 色素性隆突性皮肤纤维肉瘤(Pigmented dermatofibrosarcoma protuberans)
    8832/3 纤维肉瘤型隆突性皮肤纤维肉瘤(Dermatofibrosarcoma protuberans, fibrosarcomatous)
    黏液性隆突性皮肤纤维肉瘤(Myxoid dermatofibrosarcoma protuberans)
    隆突性皮肤纤维肉瘤伴肌样分化(Dermatofibrosarcoma protuberans with myoid differentiation)
    斑块样隆突性皮肤纤维肉瘤(Plaque-like dermatofibrosarcoma protuberans)
  • 8815/1 孤立性纤维性肿瘤NOS (Solitary fibrous tumour NOS)
    成脂性/脂防瘤样孤立性纤维性肿瘤(Fat-forming(lipomatous) solitary fibroustumour)
    巨细胞性孤立性纤维性肿瘤(Giant cell-rich solitary fibrous tumour)
  • 8825/1 炎性肌纤维母细胞性肿瘤(Inflammatory myofibroblastic tumour)
    上皮样炎性肌纤维母细胞肉瘤(Epithelioid inflammatory myofibroblastic sarcoma)
  • 8825/3 低度恶性肌纤维母细胞性肉瘤(Myofibroblastic sarcoma)
  • 8810/1 浅表性CD34阳性纤维母细胞性肿瘤(Superficial CD34-positive fibroblastic tumour)
  • 8811/1 黏液炎性纤维母细胞性肉瘤(Myxoinflammatory fibroblastic sarcoma)
  • 8814/3 婴儿纤维肉瘤(Infantile fibrosarcoma)

恶性(Malignant)

  • 8815/3 恶性孤立性纤维性肿瘤(Solitary fibrous tumour, malignant)
  • 8810/3 纤维肉瘤NOS (Fibrosarcoma NOS)
  • 8811/3 黏液纤维肉瘤(Myxofibrosarcoma)
    上皮样黏液纤维肉瘤(Epithelioid myxofibrosarcoma)
  • 8840/3 低度恶性纤维黏液样肉瘤(Low-grade fibromyxoid sarcoma)
  • 8840/3 硬化性上皮样纤维肉瘤(Sclerosing epithelioid fibrosarcoma)

所谓的纤维组织细胞性肿瘤(So-called fibrohistiocytic tumours)

良性(Benign)

  • 9252/0 腱鞘巨细胞肿瘤NOS (Tenosynovial giant cell tumour NOS)
    9252/1 腱鞘巨细胞肿瘤，弥漫型(Tenosynovial giant cell tumour, diffuse)
  • 8831/0 深部良性纤维组织细胞瘤(Deep benign fibrous histiocytoma)

中间性(偶有转移性)Intermediate(rarely metastasizing)

  • 8835/1 丛状纤维组织细胞瘤(Plexiform fibrohistiocytic tumour)
  • 9251/1 软组织巨细胞瘤(Giant cell tumour of soft parts NOS)

恶性(Malignant)

  • 9252/3 恶性腱鞘巨细胞肿瘤(Malignant tenosynovial giant cell tumour)

血管性肿瘤(Vascular tumours)

良性(Benign)

  • 9120/0 血管瘤NOS (Haemangioma NOS)
  • 9132/0 肌内血管瘤(Intramuscular haemangioma)
  • 9123/0 动静脉血管(Arteriovenous haemangioma)
  • 9122/0 静脉型血管瘤(Venous haemangioma)
  • 9125/0上皮样血管瘤(Epithelioid haemangioma)
    富于细胞上皮样血管瘤(Cellular epithelioid haemangioma)
    非典型上皮样血管瘤(Atypical epithelioid haemangioma)
  • 9170/0 淋巴管瘤NOS (Lymphangioma NOS)
    淋巴管瘤病(Lymphangiomatosis)
  • 9173/0 囊性淋巴管瘤(Cystic lymphangioma)
  • 9161/0 获得性丛状血管瘤(Acquired tufted haemangioma)

中间性(局部侵装性)Intermediate (locally aggressive)

  • 9130/1 卡波西型血管内皮瘤(Kaposiform haemangioendothelioma)

中间性(偶有转移性)Intermediate(rarely metastasizing)

  • 9136/1 网状血管内皮瘤(Retiform haemangioendothelioma)
  • 9135/1 乳头状淋巴管内血管内皮瘤(Papillary intralymphatic angioendothelioma)
  • 9136/1 复合性血管内皮瘤(Composite haemangioendothelioma)
    表达神经内分泌标记的复合性血管内皮瘤(Neuroendocrine composite haemangioendothelioma)
  • 9140/3 卡波西肉瘤(Kaposi sarcoma)
    经典型惰性卡波西肉瘤(Classic indolent Kaposi sarcoma)
    非洲地方性卡波西肉瘤(Endemic African Kaposi sarcoma)
    艾滋病相关性卡波西肉瘤(AIDS-associated Kaposi sarcoma)
    迟发型卡波西肉瘤(latrogenic Kaposi sarcoma)
  • 9138/1 假肌源性血管内皮瘤(Pseudomyogenic (epithelioidsarcoma-like)haemangioendothelioma)

恶性(Malignant)

  • 9133/3 上皮样血管内皮瘤NOS(Epithelioid haemangioendothelioma NOS)
    上皮样血管内皮瘤伴WWTR1-CAMTA1融合(Epithelioid haemangioendothelioma withWWTR1-CAMTA1 fusion)
    上皮样血管内皮瘤伴YAP1-TFE3融合(Epithelioid haemangioendothelioma withYAP1-TFE3 fusion)
  • 9120/3 血管肉瘤(Angiosarcoma)

周细胞性(血管周细胞性)肿瘤(Pericytic(perivascular) tumours)

良性和中间性(Benign and intermediate)

  • 8711/0 血管球瘤NOS (Glomus tumour NOS)
    8712/0 血管球瘤(Glomangioma)
    8713/0 血管球肌瘤(Glomangiomyoma)
    8711/1 血管球瘤病(Glomangiomatosis)
    8711/1 恶性潜能未定的血管球肿瘤(Glomus tumour of uncertain malignant potential)
  • 8824/0 肌周细胞瘤(Myopericytoma)
    8824/1 肌纤维瘤病(Myofibromatosis)
    8824/0 肌纤维瘤(Myofibroma)
    8824/1 婴儿性肌纤维瘤病(Infantile myofibromatosis)
  • 8894/0 血管平滑肌瘤(Angioleiomyoma)

恶性(Malignant)

  • 8711/3 恶性血管球瘤(Glomus tumour, malignant)

平滑肌肿瘤(Smooth muscle tumours)

良性和中间性(Benign and intermediate)

  • 8890/0 平滑肌瘤NOS(Leiomyoma NOS)
  • 8897/1 恶性潜能未定的平滑肌肿瘤(Smooth muscle tumor of uncertain malignant potential)

恶性(Malignant)

  • 8890/3 平滑肌肉瘤NOS(Leiomyosarcoma NOS)

骨骼肌肿瘤(Skeletal muscle tumours)

良性(Benign)

  • 8900/0 横纹肌瘤NOS (Rhabdomyoma NOS)
    8903/0 胎儿型横纹肌瘤(Fetal rhabdomyoma)
    8904/0 成人型横纹肌瘤(Adult rhabdomyoma)
    8905/0 生殖道型横纹肌瘤(Genital rhabdomyoma)

恶性(Malignant)

  • 8910/3 胚胎性横纹肌肉瘤NOS (Embryonal rhabdomyosarcoma NOS)
    8910/3 胚胎性横纹肌肉瘤，多形性(Embryonal rhabdomyosarcoma, pleomorphic)
  • 8920/3 腺泡状横纹肌肉瘤(Alveolar rhabdomyosarcoma)
  • 8901/3 多形性横纹肌肉瘤NOS (Pleomorphic rhabdomyosarcoma NOS)
  • 8912/3 梭形细胞/硬化性横纹肌肉瘤(Spindle cell rhabdomyosarcoma)
    先天性梭形细胞横纹肌肉瘤伴VGLL2/NCOA2/ CITED2重排(Congenital spindle cellhabdomyosarcoma with VGLL2/NCOA2/CITED2 rearrangements)
    MYOD1-突变梭形细胞/硬化性横纹肌肉瘤(MYOD1-mutant spindle cell/sclerosing rhabdomyosarcoma)
    骨内梭形细胞横纹肌肉瘤(伴TFCP2/NCOA2重排)(Intraosseous spindle cell rhabdomyosarcoma (with TFCP2/NCOA2 rearrangements))
  • 8921/3 外胚层间叶瘤(Ectomesenchymoma)

胃肠道间质瘤(Gastrointestinal stromal tumours)

  • 8936/3 胃肠道间质瘤(Gastrointestinal stromal tumour)

软骨-骨肿瘤(Chondro-osseous tumours)

良性(Benign)

  • 9220/0 软骨瘤NOS (Chondroma NOS)
    软骨母细胞样软组织软骨瘤 (Chondroblastoma-like soft tissue chondroma)

恶性(Malignant)

  • 9180/3 骨外骨肉瘤(Osteosarcoma, extraskeletal)

周围神经鞘膜肿瘤(Peripheral nerve sheath tumours)

良性(Benign)

  • 9560/0 神经鞘瘤NOS (Schwannoma NOS)
    9560/0 陈旧性神经鞘瘤(Ancient schwannoma)
    9560/0 富于细胞神经鞘瘤(Cellular schwannoma)
    9560/0 丛状神经鞘瘤(Plexiform schwannoma)
    上皮样神经鞘瘤(Epithelioid schwannoma)
    微囊/网状神经鞘瘤(Microcystic/reticular schwannoma)
  • 9540/0 神经纤维瘤NOS (Neurofibroma NOS)
    陈旧性神经纤维瘤(Ancient neurofibroma)
    富于细胞神经纤维瘤(Cellular neurofibroma)
    非典型神经纤维瘤(Atypical neurofibroma)
    9550/0 丛状神经纤维瘤(Plexiform neurofibroma)
  • 9571/0 神经束膜瘤NOS (Perineurioma NOS)
    网状神经束膜瘤(Reticular perineurioma)
    硬化性神经束膜瘤(Sclerosing perineurioma)
  • 9580/0 颗粒细胞瘤NOS (Granular cell tumour NOS)
  • 9562/0 神经鞘黏液瘤(Nerve sheath myxoma)
  • 9570/0 孤立性局限性神经瘤(Solitary circumscribed neuroma)
    丛状孤立性局限性神经瘤(Plexiform solitary circumscribed neuroma)
  • 9530/0 脑膜瘤NOS (Meningioma NOS)
  • 良性蝾螈瘤/神经肌肉迷芽瘤(Benign triton tumour /neuromuscular choristoma)
  • 9563/0 混杂性神经鞘膜瘤(Hybrid nerve sheath tumour)
    神经束膜瘤/神经鞘瘤(Perineurioma/schwannoma)
    神经鞘瘤/神经纤维瘤(Schwannoma/neurofibroma)
    神经束膜瘤/神经纤维瘤(Perineurioma/neurofibroma)

恶性(Malignant)

  • 9540/3 恶性周围神经鞘膜瘤NOS(Malignant peripheral nerve sheath tumour NOS)
    9542/3 上皮样恶性周围神经鞘膜瘤(Malignant peripheral nerve sheath tumour,epithelioid)
  • 9540/3 色素性恶性周围神经鞘膜瘤(Melanotic malignant peripheral nerve sheathtumour)
  • 9580/3 恶性颗粒细胞瘤(Granular cell tumour, malignant)
  • 9571/3 恶性神经束膜瘤(Perineurioma, malignant)

分化尚不确定的肿瘤(Tumours of uncertain differentiation)

良性(Benign)

  • 8840/0 黏液瘤NOS (Myxoma NOS)
    富于细胞黏液瘤(Cellar myxoma)
  • 8841/0 侵袭性血管黏液瘤(Aggressive angiomyxoma)
  • 8802/1 多形性玻璃样变血管扩张性肿瘤(Pleomorphic hyalinizing angiectatic tumour)
  • 8990/0 磷酸盐尿性间叶性肿瘤NOS(Phosphaturic mesenchymal tumour NOS)
  • 8714/0 良性血管周上皮样细胞肿瘤(Perivascular epithelioid tumour, benign)
  • 8860/0 血管平滑肌脂肪瘤(Angiomyolipoma)

中间性(局部侵袭性)Intermediate (locally aggressive)

  • 8811/1 含铁血黄素沉着性纤维脂肪瘤样肿瘤(Haemosiderotic fibrolipomatous tumour)
  • 8860/1 上皮样血管平滑肌脂肪瘤(Angiomyolipoma, epithelioid)

中间性(偶有转移性)Intermediate(rarely metastasizing)

  • 8830/1 非典型纤维黄色瘤(Atypical fibroxanthoma)
  • 8836/1 血管瘤样纤维组织细胞瘤(Angiomatoid fibrous histiocytoma)
  • 8842/0 骨化性纤维黏液样肿瘤(Ossifying fibromyxoid tumour NOS)
  • 8940/0 混合瘤NOS (Mixed tumour NOS)
  • 8940/3 恶性混合瘤NOS (Mixed tumour, malignant,NOS)
  • 8982/0 肌上皮瘤NOS (Myoepithelioma NOS)

恶性(Malignant)

  • 8990/3 恶性磷酸盐尿性间叶性肿瘤(Phosphaturic mesenchymal tumour, malignant)
  • NTRK重排梭形细胞肿瘤(NTRK-rearranged spindle cell neoplasm(emerging))
  • 9040/3 滑膜肉瘤NOS (Synovial sarcoma NOS)
    9041/3 滑膜肉瘤，梭形细胞型(Synovial sarcoma, spindle cell)
    9043/3 滑膜肉瘤，双相型(Synovial sarcoma, biphasic)
    滑膜肉瘤，差分化型(Synovial sarcoma, poorly differentiated)
  • 8804/3上皮样肉瘤(Epithelioid sarcoma)
    近端型或大细胞型上皮样肉瘤(Proximal or large cell epithelioid sarcoma)
    经典型(远端型)上皮样肉瘤(Classic epithelioid sarcoma)
  • 9581/3 腺泡状软组织肉瘤(Alveolar soft part sarcoma)
  • 9044/3 软组织透明细胞肉瘤(Clear cell sarcoma NOS)
  • 9231/3 骨外黏液样软骨肉瘤(Extraskeletal myxoid chondrosarcoma)
  • 8806/3 促结缔组织增生性小圆细胞肿瘤(Desmoplastic small round cell tumour)
  • 8963/3 恶性肾外横纹肌样瘤(Rhabdoid tumour NOS)
  • 8714/3 恶性血管周上皮样细胞肿瘤(Perivascular epithelioid tumour, malignant)
  • 9137/3 (动脉)内膜肉瘤(Intimal sarcoma)
  • 8842/3 骨化性纤维黏液样肿瘤，恶性(Ossifying fibromyxoid tumour, malignant)
  • 8982/3 肌上皮癌(Myoepithelial carcinoma)
  • 8805/3 未分化肉瘤(Undifferentiated sarcoma)
  • 8801/3 梭形细胞肉瘤，未分化 (Spindle cell sarcoma, undifferentiated)
  • 8802/3 多形性肉瘤，未分化(Pleomorphic sarcoma, undifferentiated)
  • 8803/3 圆形细胞肉瘤，未分化(Round cell sarcoma, undifferentiated)

软组织和骨未分化小圆细胞肉瘤(Undifferentiated small round cell sarcomas of bone and soft tissue)

  • 9364/3 尤因肉瘤(Ewing sarcoma)
  • 9366/3 伴有EWSR1-非ETS家族融合基因的圆细胞肉瘤(Round cell sarcoma with EWSR1-non ETS fusions)
  • 9367/3 CIC重排肉瘤(CIC-rearranged sarcoma)
  • 9368/3 伴有BCOR遗传学改变的肉瘤(Sarcoma with BCOR genetic alteration)